Nature

Respiratory bronchiolitis-associated interstitial lung disease with fibrosis is a lesion distinct from fibrotic nonspecific interstitial pneumonia: a proposal

The consultation files of the author were searched for all cases referred to the author in consultation as possible ‘nonspecific interstitial pneumonia’ from 2000 to 2006. Of these 32 cases, nine ...
Nature

Nonspecific Interstitial Pneumonia, Alveolar Proteinosis, and Abnormal Proprotein Trafficking Resulting from a Spontaneous Mutation in the Surfactant Protein C Gene

Pulmonary surfactant is a biochemically heterogeneous surface-active mixture of phospholipids and proteins secreted into the alveolar space by type II epithelial cells (1). Formation of the surfactant ...